| Single-dose gene-replacement therapy for spinal muscular atrophy JR Mendell, S Al-Zaidy, R Shell, WD Arnold, LR Rodino-Klapac, TW Prior, ... New England Journal of Medicine 377 (18), 1713-1722, 2017 | 2069 | 2017 |
| Astrocytes from familial and sporadic ALS patients are toxic to motor neurons AM Haidet-Phillips, ME Hester, CJ Miranda, K Meyer, L Braun, A Frakes, ... Nature biotechnology 29 (9), 824-828, 2011 | 898 | 2011 |
| Microglia induce motor neuron death via the classical NF-κB pathway in amyotrophic lateral sclerosis AE Frakes, L Ferraiuolo, AM Haidet-Phillips, L Schmelzer, L Braun, ... Neuron 81 (5), 1009-1023, 2014 | 650 | 2014 |
| Direct conversion of patient fibroblasts demonstrates non-cell autonomous toxicity of astrocytes to motor neurons in familial and sporadic ALS K Meyer, L Ferraiuolo, CJ Miranda, S Likhite, S McElroy, S Renusch, ... Proceedings of the National Academy of Sciences 111 (2), 829-832, 2014 | 384 | 2014 |
| Rapid and efficient generation of functional motor neurons from human pluripotent stem cells using gene delivered transcription factor codes ME Hester, MJ Murtha, SW Song, M Rao, CJ Miranda, K Meyer, J Tian, ... Molecular therapy 19 (10), 1905-1912, 2011 | 222 | 2011 |
| Trinucleotide repeats in 202 families with ataxia: a small expanded (CAG) n allele at the SCA17 locus I Silveira, C Miranda, L Guimaraes, MC Moreira, I Alonso, P Mendonca, ... Archives of neurology 59 (4), 623-629, 2002 | 203 | 2002 |
| Oligodendrocytes contribute to motor neuron death in ALS via SOD1-dependent mechanism L Ferraiuolo, K Meyer, TW Sherwood, J Vick, S Likhite, A Frakes, ... Proceedings of the National Academy of Sciences 113 (42), E6496-E6505, 2016 | 194 | 2016 |
| Frataxin knockin mouse CJ Miranda, MM Santos, K Ohshima, J Smith, L Li, M Bunting, M Cossée, ... FEBS letters 512 (1-3), 291-297, 2002 | 191 | 2002 |
| Hfe deficiency increases susceptibility to cardiotoxicity and exacerbates changes in iron metabolism induced by doxorubicin CJ Miranda, H Makui, RJ Soares, M Bilodeau, J Mui, H Vali, R Bertrand, ... Blood 102 (7), 2574-2580, 2003 | 179 | 2003 |
| Aging brain microenvironment decreases hippocampal neurogenesis through Wnt‐mediated survivin signaling CJ Miranda, L Braun, Y Jiang, ME Hester, L Zhang, M Riolo, H Wang, ... Aging cell 11 (3), 542-552, 2012 | 171 | 2012 |
| Chronic oligodendrogenesis and remyelination after spinal cord injury in mice and rats ZC Hesp, EA Goldstein, CJ Miranda, BK Kaspar, DM McTigue Journal of Neuroscience 35 (3), 1274-1290, 2015 | 169 | 2015 |
| Produção de briquetes e péletes a partir de resíduos agrícolas, agroindustriais e florestais. JMCS Dias, DT Dos Santos, M BRAGA, MM ONOYAMA, CHB MIRANDA, ... Brasília, DF: Embrapa Agroenergia, 2012., 2012 | 155 | 2012 |
| Major histocompatibility complex class I molecules protect motor neurons from astrocyte-induced toxicity in amyotrophic lateral sclerosis SW Song, CJ Miranda, L Braun, K Meyer, AE Frakes, L Ferraiuolo, ... Nature medicine 22 (4), 397-403, 2016 | 140 | 2016 |
| NEUROD1 instructs neuronal conversion in non-reactive astrocytes R Brulet, T Matsuda, L Zhang, C Miranda, M Giacca, BK Kaspar, ... Stem cell reports 8 (6), 1506-1515, 2017 | 127 | 2017 |
| Unique origin and specific ethnic distribution of the Friedreich ataxia GAA expansion M Labuda, D Labuda, C Miranda, J Poirier, BW Soong, NE Barucha, ... Neurology 54 (12), 2322-2324, 2000 | 116 | 2000 |
| Human CFEOM1 mutations attenuate KIF21A autoinhibition and cause oculomotor axon stalling L Cheng, J Desai, CJ Miranda, JS Duncan, W Qiu, AA Nugent, AL Kolpak, ... Neuron 82 (2), 334-349, 2014 | 106 | 2014 |
| Two factor reprogramming of human neural stem cells into pluripotency ME Hester, SW Song, CJ Miranda, A Eagle, PH Schwartz, BK Kaspar PloS one 4 (9), e7044, 2009 | 88 | 2009 |
| Gene expression profiling in frataxin deficient mice: microarray evidence for significant expression changes without detectable neurodegeneration G Coppola, SH Choi, MM Santos, CJ Miranda, D Tentler, EM Wexler, ... Neurobiology of disease 22 (2), 302-311, 2006 | 64 | 2006 |
| Genomic structure, promoter activity, and developmental expression of the mouse homologue of the Machado–Joseph disease (MJD) gene M do Carmo Costa, J Gomes-da-Silva, CJ Miranda, J Sequeiros, ... Genomics 84 (2), 361-373, 2004 | 49 | 2004 |
| Frataxin overexpressing mice CJ Miranda, MM Santos, K Ohshima, M Tessaro, J Sequeiros, M Pandolfo FEBS letters 572 (1-3), 281-288, 2004 | 40 | 2004 |
Jorge SequeirosICBAS; UnIGENe and CGPP, IBMC / i3S; Universidade do PortoVerified email at ibmc.up.pt
