|Guidelines for the use and interpretation of assays for monitoring autophagy (4th edition)1|
DJ Klionsky, AK Abdel-Aziz, S Abdelfatah, M Abdellatif, A Abdoli, S Abel, ...
autophagy 17 (1), 1-382, 2021
|Transgenics, toxicity and therapeutics in rodent models of mutant SOD1-mediated familial ALS|
BJ Turner, K Talbot
Progress in neurobiology 85 (1), 94-134, 2008
|Intercellular propagated misfolding of wild-type Cu/Zn superoxide dismutase occurs via exosome-dependent and-independent mechanisms|
LI Grad, JJ Yerbury, BJ Turner, WC Guest, E Pokrishevsky, MA O’Neill, ...
Proceedings of the National Academy of Sciences 111 (9), 3620-3625, 2014
|Induction of the unfolded protein response in familial amyotrophic lateral sclerosis and association of protein-disulfide isomerase with superoxide dismutase 1|
JD Atkin, MA Farg, BJ Turner, D Tomas, JA Lysaght, J Nunan, A Rembach, ...
Journal of Biological Chemistry 281 (40), 30152-30165, 2006
|Impaired extracellular secretion of mutant superoxide dismutase 1 associates with neurotoxicity in familial amyotrophic lateral sclerosis|
BJ Turner, JD Atkin, MA Farg, A Rembach, EC Lopes, JD Patch, AF Hill, ...
Journal of Neuroscience 25 (1), 108-117, 2005
|Emerging therapies and challenges in spinal muscular atrophy|
MA Farrar, SB Park, S Vucic, KA Carey, BJ Turner, TH Gillingwater, ...
Annals of neurology 81 (3), 355-368, 2017
|TDP-43 triggers mitochondrial DNA release via mPTP to activate cGAS/STING in ALS|
CH Yu, S Davidson, CR Harapas, JB Hilton, MJ Mlodzianoski, ...
Cell 183 (3), 636-649. e18, 2020
|The bone morphogenetic protein axis is a positive regulator of skeletal muscle mass|
CE Winbanks, JL Chen, H Qian, Y Liu, BC Bernardo, C Beyer, KI Watt, ...
Journal of Cell Biology 203 (2), 345-357, 2013
|ALS-associated TDP-43 induces endoplasmic reticulum stress, which drives cytoplasmic TDP-43 accumulation and stress granule formation|
AK Walker, KY Soo, V Sundaramoorthy, S Parakh, Y Ma, MA Farg, ...
PloS one 8 (11), e81170, 2013
|Oral treatment with CuII (atsm) increases mutant SOD1 in vivo but protects motor neurons and improves the phenotype of a transgenic mouse model of amyotrophic lateral sclerosis|
BR Roberts, NKH Lim, EJ McAllum, PS Donnelly, DJ Hare, PA Doble, ...
Journal of Neuroscience 34 (23), 8021-8031, 2014
|Diacetylbis (N (4)-methylthiosemicarbazonato) copper (II)(CuII (atsm)) protects against peroxynitrite-induced nitrosative damage and prolongs survival in amyotrophic lateral …|
CPW Soon, PS Donnelly, BJ Turner, LW Hung, PJ Crouch, NA Sherratt, ...
Journal of Biological Chemistry 286 (51), 44035-44044, 2011
|Antisense peptide nucleic acid‐mediated knockdown of the p75 neurotrophin receptor delays motor neuron disease in mutant SOD1 transgenic mice|
BJ Turner, IK Cheah, KJ Macfarlane, EC Lopes, S Petratos, SJ Langford, ...
Journal of neurochemistry 87 (3), 752-763, 2003
|The Hippo pathway effector YAP is a critical regulator of skeletal muscle fibre size|
KI Watt, BJ Turner, A Hagg, X Zhang, JR Davey, H Qian, C Beyer, ...
Nature communications 6 (1), 1-13, 2015
|Disease mechanisms in ALS: misfolded SOD1 transferred through exosome-dependent and exosome-independent pathways|
JM Silverman, SM Fernando, LI Grad, AF Hill, BJ Turner, JJ Yerbury, ...
Cellular and molecular neurobiology 36 (3), 377-381, 2016
|Mutant SOD 1 inhibits ER‐Golgi transport in amyotrophic lateral sclerosis|
JD Atkin, MA Farg, KY Soo, AK Walker, M Halloran, BJ Turner, P Nagley, ...
Journal of neurochemistry 129 (1), 190-204, 2014
|Association of regulatory T-cell expansion with progression of amyotrophic lateral sclerosis: a study of humans and a transgenic mouse model|
RK Sheean, FC McKay, E Cretney, CR Bye, ND Perera, D Tomas, ...
JAMA neurology 75 (6), 681-689, 2018
|Survival motor neuron deficiency enhances progression in an amyotrophic lateral sclerosis mouse model|
BJ Turner, NJ Parkinson, KE Davies, K Talbot
Neurobiology of disease 34 (3), 511-517, 2009
|ER stress and UPR in familial amyotrophic lateral sclerosis|
BJ Turner, JD Atkin
Current molecular medicine 6 (1), 79-86, 2006
|Dysregulation of the complement cascade in the hSOD1G93Atransgenic mouse model of amyotrophic lateral sclerosis|
JD Lee, NA Kamaruzaman, JNT Fung, SM Taylor, BJ Turner, JD Atkin, ...
Journal of neuroinflammation 10 (1), 1-15, 2013
|SOD1 protein aggregates stimulate macropinocytosis in neurons to facilitate their propagation|
R Zeineddine, JF Pundavela, L Corcoran, EM Stewart, D Do-Ha, M Bax, ...
Molecular neurodegeneration 10 (1), 1-18, 2015