Matthew McKenzie PhD
Matthew McKenzie PhD
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Mitochondrial respiratory chain supercomplexes are destabilized in Barth Syndrome patients
M McKenzie, M Lazarou, DR Thorburn, MT Ryan
Journal of molecular biology 361 (3), 462-469, 2006
Understanding mitochondrial complex I assembly in health and disease
M Mimaki, X Wang, M McKenzie, DR Thorburn, MT Ryan
Biochimica et Biophysica Acta (BBA)-Bioenergetics 1817 (6), 851-862, 2012
Analysis of the assembly profiles for mitochondrial-and nuclear-DNA-encoded subunits into complex I
M Lazarou, M McKenzie, A Ohtake, DR Thorburn, MT Ryan
Molecular and cellular biology 27 (12), 4228-4237, 2007
Mutation of the mitochondrial tyrosyl-tRNA synthetase gene, YARS2, causes myopathy, lactic acidosis, and sideroblastic anemia—MLASA syndrome
LG Riley, S Cooper, P Hickey, J Rudinger-Thirion, M McKenzie, ...
The American Journal of Human Genetics 87 (1), 52-59, 2010
Mitochondrial cardiolipin involved in outer-membrane protein biogenesis: implications for Barth syndrome
N Gebert, AS Joshi, S Kutik, T Becker, M McKenzie, XL Guan, VP Mooga, ...
Current biology 19 (24), 2133-2139, 2009
Assembly of mitochondrial complex I and defects in disease
M Lazarou, DR Thorburn, MT Ryan, M McKenzie
Biochimica et Biophysica Acta (BBA)-Molecular Cell Research 1793 (1), 78-88, 2009
Human CIA30 is involved in the early assembly of mitochondrial complex I and mutations in its gene cause disease
CJR Dunning, M McKenzie, C Sugiana, M Lazarou, J Silke, A Connelly, ...
The EMBO journal 26 (13), 3227-3237, 2007
Mitochondrial DNA copy number is regulated in a tissue specific manner by DNA methylation of the nuclear-encoded DNA polymerase gamma A
RDW Kelly, A Mahmud, M McKenzie, IA Trounce, JC St John
Nucleic acids research 40 (20), 10124-10138, 2012
Mutation of C20orf7 disrupts complex I assembly and causes lethal neonatal mitochondrial disease
C Sugiana, DJ Pagliarini, M McKenzie, DM Kirby, R Salemi, ...
The American Journal of Human Genetics 83 (4), 468-478, 2008
Mutations in MTFMT underlie a human disorder of formylation causing impaired mitochondrial translation
EJ Tucker, SG Hershman, C Köhrer, CA Belcher-Timme, J Patel, ...
Cell metabolism 14 (3), 428-434, 2011
Assembly factors of human mitochondrial complex I and their defects in disease
M Mckenzie, MT Ryan
IUBMB life 62 (7), 497-502, 2010
The regulation of mitochondrial DNA copy number in glioblastoma cells
A Dickinson, KY Yeung, J Donoghue, MJ Baker, RDW Kelly, M McKenzie, ...
Cell Death & Differentiation 20 (12), 1644-1653, 2013
Mitochondrial disease: mutations and mechanisms
M McKenzie, D Liolitsa, MG Hanna
Neurochemical research 29, 589-600, 2004
Combined defects in oxidative phosphorylation and fatty acid β-oxidation in mitochondrial disease
A Nsiah-Sefaa, M McKenzie
Bioscience reports 36 (2), e00313, 2016
Functional Respiratory Chain Analyses in Murid Xenomitochondrial Cybrids Expose Coevolutionary Constraints of Cytochrome b and Nuclear Subunits of Complex III
M McKenzie, M Chiotis, CA Pinkert, IA Trounce
Molecular Biology and Evolution 20 (7), 1117-1124, 2003
Analysis of mitochondrial subunit assembly into respiratory chain complexes using Blue Native polyacrylamide gel electrophoresis
M McKenzie, M Lazarou, DR Thorburn, MT Ryan
Analytical biochemistry 364 (2), 128-137, 2007
Assembly of nuclear DNA‐encoded subunits into mitochondrial complex IV, and their preferential integration into supercomplex forms in patient mitochondria
M Lazarou, SM Smith, DR Thorburn, MT Ryan, M McKenzie
The FEBS journal 276 (22), 6701-6713, 2009
Integrating mitochondrial aerobic metabolism into ecology and evolution
RE Koch, KL Buchanan, S Casagrande, O Crino, DK Dowling, GE Hill, ...
Trends in Ecology & Evolution 36 (4), 321-332, 2021
Expression of Rattus Norvegicus MtDNA InMus Musculus Cells Results in Multiple Respiratory Chain Defects
M McKenzie, I Trounce
Journal of Biological Chemistry 275 (40), 31514-31519, 2000
Restoration of normal embryogenesis by mitochondrial supplementation in pig oocytes exhibiting mitochondrial DNA deficiency
GLM Cagnone, TS Tsai, Y Makanji, P Matthews, J Gould, MS Bonkowski, ...
Scientific reports 6 (1), 23229, 2016
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